KA Aly Mbara1*, DIAGNE Jean Pierre1, DIENG Mamour3, GUEYE Abou1, SOW Aboubacry Sadekh2, SY El Hadji Malick1, NDIAYE Joseph Matar Mass2, MBAYE Soda1, DE MEIDEROS Marguerite Edith Quenum1, SAMRA Audrey1, GAYE Serigne Sohibou1, BADGI Mariama2, WANE Aissatou Magatte3 and NDIAYE Papa Amadou1
1Abass Ndao National Hospital Eye Center, Senegal 2Department of Ophthalmology, Hospital Center University Aristide Le Dantec, Senegal 3Department of Ophthalmology, Diamniadio Children’s Hospital, SenegalFulltext PDF
Aim: in order to underline the rarity as well as the diagnostic, therapeutic and prognostic aspects of this affection, we report one case of an embryonic orbital rhabdomyosarcoma in a newborn. Observation: It was a 3 months-old female baby, full-term by vaginal delivery, of a well-followed pregnancy. The mother was 19-years old, primigravida, primiparous and without parental inbreeding. The baby was admitted at the 5th day of life for a left exorbitism at her birth. Examination found a tumoral orbital syndrome with a beginning corneal necrosis. A head CT-scan found a dense tissue process occupying the left orbit and discharging the orbital content outside, with a contrast enhancement. It was developed on medial rectus muscle. The alpha-fetoprotein level at 8th day of life was high, about 400 ng/ml. An exaltation was realized at the 9th day of life with a pathological examination evoking a rhabdomyosarcoma. After a month and a half, there was a tumor recurrence. The blood smear showed more than 25% of blasts. The baby has received courses of chemotherapy. Discussion and Conclusion: The diagnosis of rhabdomyosarcoma must be evoked in any child with orbital evolutive signs. An imaging must be performed urgently. The embryonal form is the more common, but its occurrence in newborn period is particular.
Rhabdomyosarcoma; Newborn; Vital prognosis
Ka AM, Diagne JP, Dieng M, Gueye A, Sow AS, Sy EM, and et al. About One Case of Primitive Embryonal Rhabdomyosarcoma. J Clin Ophthalmol Eye Disord. 2022; 6(1): 1041..