Ann Cardiol Cardiovasc Med | Volume 5, Issue 1 | Case Report | Open Access

Congenital Complete Heart Block in Congenitally Corrected Transposition of the Great Arteries

Anna Ulfah Rahajoe1*, Radityo Prakoso1, Muhammad Rizky Felani1, Yovi Kurniawati1, Oktavia Lilyasari1, Dicky Hanafy2, Novik Budiwardhana3 and Salomo Purba4

1Department of Cardiology and Vascular Medicine, Universitas Indonesia, Division of Pediatric Cardiology and Congenital Heart Disease, National Cardiovascular Center Harapan Kita, Indonesia
2Department of Cardiology and Vascular Medicine, Universitas Indonesia, Division of Arrhythmia, National Cardiovascular Center Harapan Kita, Indonesia
3Division of Pediatric Cardiac Intensive Care Unit, National Cardiovascular Center Harapan Kita, Indonesia
4Division of Pediatric and Congenital Heart Surgery, National Cardiovascular Center Harapan Kita, Indonesia

*Correspondance to: Anna Ulfah Rahajoe 

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Background: Congenital complete Heart Block (CHB) in patient with Congenitally Corrected Transposition of the Great Arteries (CCTGA) is extremely rare.
Case Summary: A premature 2-days-old baby was referred with hypotension and bradycardia detected in utero. Electrocardiograph showed complete heart block with junctional escape rhythm of 71/min and features of ventricular inversion. Cardiomegaly was seen on chest X-ray and the laboratory findings suggesting sepsis with hyperbilirubinemia. Two-dimensional echocardiography revealed CCTGA. Transvenous Temporary Pacemaker (TPM) was inserted immediately in the Right
Ventricle (RV) endocardium, followed by VVI pacemaker implantation at the RV epicardium. The patient was discharged in full recovery.
Discussion: A planned antenatal monitoring, delivery and early referral can lead to favorable outcomes, however, a lifelong follow up for RV function worsening, progressive tricuspid regurgitation, and epicardial pacemaker side effects is important, this might be a problem for patients who live in countries with limited resources.


Complete heart block; Congenitally corrected transposition of great arteries; Neonate; Epicardial pacemaker


Rahajoe AU, Prakoso R, Felani MR, Kurniawati Y, Lilyasari O, Hanafy D, et al. Congenital Complete Heart Block in Congenitally Corrected Transposition of the Great Arteries. Ann Cardiol Cardiovasc Med. 2021;5(1):1044..

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