Am J Otolaryngol Head Neck Surg | Volume 2, Issue 9 | Case Report | Open Access

Transoral Robotic Excision of Hemangioma Tongue in Rare Case of Maffucci Syndrome

Kalpana Nagpal^1*, Noor-Ul-Din Malik¹, Kamal Goyal¹, Ansari SH¹, Venus Rawat¹ and Vikas Kashyap²

¹Department of ENT, Head and Neck Surgery and Robotic Surgery, Indraprastha Apollo Hospital, India
²Department of Pathology, Indraprastha Apollo Hospital, India

^*Correspondance to: Kalpana Nagpal 

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Abstract

Maffucci syndrome is an extremely rare disorder characterized by benign overgrowths of cartilage (enchondromas), skeletal deformities and cutaneous lesions composed of abnormal blood vessels (hemangioma). Enchondromas arise in bones, most frequently in the hands and feet, and less often in the legs and long bones of the arm. We present a case report of hemangioma right side base of tongue and operated enchondroma left foot labelled as Maffucci syndrome. Patient underwent MRI contrast neck and after confirming the diagnosis, patient underwent robotic tongue base excision of hemangioma. No blood transfusion was required as robotic surgery is minimally invasive with minimal bleeding. Patient stay in hospital was only 1 day and recovered completely after the surgery and is doing well currently with no recurrence.

Keywords:

Maffucci syndrome; Hemangioma tongue; Transoral robotic surgery

Citation:

Nagpal K, Noor-Ul-Din Malik, Goyal K, Ansari SH, Rawat V, Kashyap V. Transoral Robotic Excision of Hemangioma Tongue in Rare Case of Maffucci Syndrome. Am J Otolaryngol Head Neck Surg. 2019; 2(9): 1071.