J Pediatr Res | Volume 4, Issue 2 | Case Report | Open Access

Pulmonary Artery Agenesis: A Rare Case Report

Tahir Tok1*, Muhammmed Burak Selver1, Amet Yasin Guney1 and Sevgi Pekcan2

1Department of Pediatrics, Necmettin Erbakan University, Turkey 2Department of Pediatric Pulmonology, Necmettin Erbakan University, Turkey

*Correspondance to: Tahir Tok 

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Pulmonary artery agenesis is one of the rare anomalies of unknown etiology and approximately 50% can be associated with congenital malformations such as cardiovascular, gastrointestinal, neuromusculoskeletal and genitourinary system. Pulmonary artery agenesis is a rare congenital anomaly in neonatal period or later in life. It often causes respiratory distress syndrome in the neonatal period. Differential diagnosis includes total atelectasis, congenital diaphragmatic hernia, congenital cystic adenomatoid malformation, pulmonary sequestration, chylothorax, pneumothorax, bronchogenic cyst and soft tissue tumors. Computed tomography is the preferred imaging method for diagnosis. Prognosis depends on the presence of other concomitant anomalies and functional capacity of the lung. We detected right pulmonary artery agenesis in a patient with recurrent lung infection. Because of the vital importance of early diagnosis in these patients, we aimed to draw attention to such variation diseases.


Pulmonary artery agenesis; Child; Recurrent pneumonia


Tok T, Selver MB, Guney AY, Pekcan S. Pulmonary Artery Agenesis: A Rare Case Report. Ann Pediatr Res. 2020;4(2):1038..

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