Ann Pain Med | Volume 3, Issue 1 | Case Series | Open Access

Chronic Pain Management in the Patients with Torg-Winchester Syndrome and Anesthesia Experience at Home

Sevgi Ballı Seyhan1* and Hoshanc Sdeeq Rashid2

1Department of Anesthesiology and Reanimation, Sehit Sait Erturk Government Hospital, Turkey
2Department of Neurosurgery, West Emergency Hospital, Iraq

*Correspondance to: Sevgi Ballı Seyhan 

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Abstract

Torg-Winchester Syndrome is characterized by diffuse osteolysis, severe osteoporosis, progressive arthropathy of the joints, contracture and hard, multiple, painless, subcutaneous nodules. Patients also have hypertrichosis, skin hyperpigmentation, corneal opacities, gingiva hypertrophy, rough facial appearance and thickened skin. In this autosomal recessive syndrome, Matrix Metalloproteinase-2 (MMP2) mutation is present. Patients with Torg-Winchester Syndrome may have severe pain. The analgesia of these patients is difficult, but should not be neglected. It should be noted that there may be a difficult airway when there is a need for analgesia and anesthesia. In our country, only 2 male patients (siblings) are diagnosed in Torg-Winchester Syndrome, which is in autosomal recessive and rare diseases group. Only a few cases have been reported in the medical literature till now. This syndrome is very rare and unusual; less literature related to anesthesia management, the problems of these patients and their approach were presented.

Keywords:

Torg-Winchester syndrome; Anesthesia at home; Pain management

Citation:

Seyhan SB, Rashid HS. Chronic Pain Management in the Patients with Torg-Winchester Syndrome and Anesthesia Experience at Home. Annals Pain Med. 2021;3(1):1010..

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