Vessel Kantardjiev1, Kristina Petkova1 and Valentina Broshtilova1,2*
1Department of Dermatology and Venereology, Military Medical Academy, Bulgaria 2Department of Infectious Diseases, Parasitology and Dermatovenereology, Medical University Prof. Dr Paraskev Stoyanov, BulgariaFulltext PDF
Mastocytosis is a rare condition characterized by a progressive accumulation of mast cells in cutaneous tissue and extracutaneous organs. The skin is involved in the majority of cases, hence, presented with heterogenic clinical expression. No more than 50 patients with anetodermic mastocytosis have been reported worldwide, most of which were adults. Herein, an anecdotal case of a 7-yearold patient with disseminated anetodermic lesions and cicatricial alopecia, histological verified as mastocytosis, is presented. Remarkably, Darier’s sign, usually pathognomic for mastocytosis, was negative. PUVA treatment was considered the right choice of treatment. A comprehensive review of literature demonstrates the very rare nature of the disease and the exceptional involvement of the scalp in this age group.
Anetoderma; Mastocytosis; Cicatricial alopecia
Kantardjiev V, Petkova K, Broshtilova V. Cicatricial Alopecia in a Pediatric Patient with Anetodermic Mastocytosis. Ann Clin Case Rep. 2019; 4: 1778.